139 1 VLAB _Label1 1 1 30 0 0 0 0 112 +===========================================================+=================== _Label2 81 1 30 0 0 0 0 112 ==============================================+========================= _Label3 1 2 30 0 0 0 0 112 ========== PACIFIC ISLANDS RHD GENETICS NETWORK _Label4 81 2 30 0 0 0 0 112 ========== _Label5 1 3 30 0 0 0 0 112 ========== | CASE CRF v2.5 | ======== _Label6 81 3 30 0 0 0 0 112 == _Label7 1 4 30 0 0 0 0 112 +===================================================== _Label8 81 4 30 0 0 0 0 112 ================+ _Label9 1 6 30 0 0 0 0 112 ===========+==================================+==============+================== _Label10 81 6 30 0 0 0 0 112 ======================================================================= _Label11 1 7 30 0 0 0 0 112 var | Question | Entry | Legal _Label12 81 7 30 0 0 0 0 112 Entries _Label13 1 8 30 0 0 0 0 112 ===========+==================================+==============+================== _Label14 81 8 30 0 0 0 0 112 ======================================================================= #UID 1 11 30 50 11 0 7 112 UID Unique Identifier : _Label15 57 11 30 0 0 0 0 112 seven digit number #STATUS 1 13 30 50 13 0 1 112 STATUS Case-Control Status : _Label16 51 13 30 0 0 0 0 112 0 = Control 1 = Case #SEX 1 15 30 50 15 0 1 112 SEX Sex : _Label17 51 15 30 0 0 0 0 112 0 = Male 1 = Female 9 = Unknown #COUNTRY 1 17 30 50 17 0 1 112 COUNTRY Country : _Label18 51 17 30 0 0 0 0 112 1 = Fiji 2 = New Caledonia #ETHNICI 1 19 30 50 19 0 1 112 ETHNICI Reported Ethnicity : _Label19 51 19 30 0 0 0 0 112 1 = iTaukei (Indigenous Fijian) 2 = Indo-Fiji _Label20 131 19 30 0 0 0 0 112 an _Label21 1 20 30 0 0 0 0 112 _Label22 81 20 30 0 0 0 0 112 3 = Other Pacific Islander 4 = Other Asian _Label23 1 21 30 0 0 0 0 112 _Label24 81 21 30 0 0 0 0 112 5 = Caucasian 6 = Mixed or Other #YOB 1 23 30 50 23 0 4 112 YOB Year of Birth : #YEARDIAGN 1 25 30 50 25 0 4 112 YEARDIAGN Year of diagnosis? : _Label25 54 25 30 0 0 0 0 112 9999 = Unknown #DIAGNOS 1 27 30 50 27 0 1 112 DIAGNOS Headline RHD diagnosis? : _Label26 51 27 30 0 0 0 0 112 1 = RHD based on surgical findings _Label27 1 28 30 0 0 0 0 112 _Label28 81 28 30 0 0 0 0 112 2 = RHD based on MS with MV area less than 2.0 cm^2 _Label29 1 29 30 0 0 0 0 112 _Label30 81 29 30 0 0 0 0 112 3 = RHD based on MS with mean gradient >> 4 mmHg _Label31 1 30 30 0 0 0 0 112 _Label32 81 30 30 0 0 0 0 112 4 = Definite RHD based on WHF echo criteria _Label33 1 31 30 0 0 0 0 112 _Label34 81 31 30 0 0 0 0 112 5 = Borderline RHD based on WHF criteria and ARF _Label35 1 33 30 0 0 0 0 112 =========== Echocardiographic features where diagnosis was echocardiographic: == _Label36 81 33 30 0 0 0 0 112 ======================================================================= #ECHODEFIN 1 35 30 50 35 0 1 112 ECHODEFIN Definite diagnostic category by WHF? : _Label37 51 35 30 0 0 0 0 112 1 = Pathological MR with >> 2 morphological feat _Label38 131 35 30 0 0 0 0 112 ures of RHD of the MV _Label39 1 36 30 0 0 0 0 112 _Label40 81 36 30 0 0 0 0 112 2 = Pathological AR and >> 2 morphological features of RHD of the MV _Label41 1 37 30 0 0 0 0 112 _Label42 81 37 30 0 0 0 0 112 3 = Pathological AR with >> 2 morphological features of RHD of the AV _Label43 1 38 30 0 0 0 0 112 _Label44 81 38 30 0 0 0 0 112 4 = Pathological MR and pathological AR #ECHOBORDR 1 40 30 50 40 0 1 112 ECHOBORDR Diagnostic category for borderline? : _Label45 51 40 30 0 0 0 0 112 1 = At least two morphological features of RHD o _Label46 131 40 30 0 0 0 0 112 f the MV without pathological MR or MS _Label47 1 41 30 0 0 0 0 112 _Label48 81 41 30 0 0 0 0 112 2 = Pathological MR _Label49 1 42 30 0 0 0 0 112 _Label50 81 42 30 0 0 0 0 112 3 = Pathological AR _Label51 1 44 30 0 0 0 0 112 ---> Morphologic features at MV? 0 = No _Label52 81 44 30 0 0 0 0 112 1 = Yes #MPHOMVTHI 1 45 30 50 45 0 1 112 MPHOMVTHI AMVL thickening (age-specific) : #MPHOMVCHR 1 46 30 50 46 0 1 112 MPHOMVCHR Chordal thickening : #MPHOMVRES 1 47 30 50 47 0 1 112 MPHOMVRES Restricted leaflet motion : #MPHOMVTIP 1 48 30 50 48 0 1 112 MPHOMVTIP Excessive leaflet tip motion : #MPHOMVFLA 1 49 30 50 49 0 1 112 MPHOMVFLA Flail in age less than years : _Label53 1 51 30 0 0 0 0 112 ---> Morphological features at AV? 0 = No _Label54 81 51 30 0 0 0 0 112 1 = Yes #MPHOAVTHI 1 52 30 50 52 0 1 112 MPHOAVTHI Irregular or focal thickening : #MPHOAVCOA 1 53 30 50 53 0 1 112 MPHOAVCOA Coaptation defect : #MPHOAVRES 1 54 30 50 54 0 1 112 MPHOAVRES Restricted leaflet motion : #MPHOAVPRO 1 55 30 50 55 0 1 112 MPHOAVPRO Prolapse : #ECHODATE 1 57 30 50 57 0 4 112 ECHODATE Year of last echocardiogram? : _Label55 54 57 30 0 0 0 0 112 9999 = Unknown _Label56 1 59 30 0 0 0 0 112 =========== Clinical and echocardiographic features of severity: =============== _Label57 81 59 30 0 0 0 0 112 ======================================================================= #NYHASCORE 1 61 30 50 61 0 1 112 NYHASCORE Symptomatic heart failure? : _Label58 51 61 30 0 0 0 0 112 1 = NYHA I 2 = NYHA II 3 = NYHA III 4 = _Label59 131 61 30 0 0 0 0 112 NYHA IV 9 = Unknown #SEVMR 1 63 30 50 63 0 1 112 SEVMR Mitral regurg. report? : _Label60 51 63 30 0 0 0 0 112 0 = None 1 = Mild 2 = Moderate 3 = Severe 9 = Unknow _Label61 131 63 30 0 0 0 0 112 n #SEVMS 1 64 30 50 64 0 1 112 SEVMS Mitral stenosis report? : _Label62 51 64 30 0 0 0 0 112 0 = None 1 = Mild 2 = Moderate 3 = Severe 9 = Unknow _Label63 131 64 30 0 0 0 0 112 n #SEVAR 1 65 30 50 65 0 1 112 SEVAR Aortic regurg. report? : _Label64 51 65 30 0 0 0 0 112 0 = None 1 = Mild 2 = Moderate 3 = Severe 9 = Unknow _Label65 131 65 30 0 0 0 0 112 n #SEVAS 1 66 30 50 66 0 1 112 SEVAS Aortic stenosis report? : _Label66 51 66 30 0 0 0 0 112 0 = None 1 = Mild 2 = Moderate 3 = Severe 9 = Unknow _Label67 131 66 30 0 0 0 0 112 n #SEVTR 1 67 30 50 67 0 1 112 SEVTR Tricupsid regurg. report? : _Label68 51 67 30 0 0 0 0 112 0 = None 1 = Mild to moderate 2 = Severe 9 = Unknow _Label69 131 67 30 0 0 0 0 112 n #SEVLVEF 1 69 30 50 69 0 1 112 SEVLVEF LV systolic EF less than 60%? : _Label70 51 69 30 0 0 0 0 112 0 = No _Label71 1 70 30 0 0 0 0 112 1 = Yes _Label72 1 71 30 0 0 0 0 112 9 = Unknown _Label73 1 73 30 0 0 0 0 112 =========== Clinical features at presentation and complications: =============== _Label74 81 73 30 0 0 0 0 112 ======================================================================== _Label75 1 75 30 0 0 0 0 112 ---> Clinical features at presentation? 0 = No _Label76 81 75 30 0 0 0 0 112 1 = Yes #PRESJONES 1 76 30 40 76 0 1 112 PRESJONES ARF (Jones Crit. Definite) : #PRESARF 41 76 30 89 76 0 1 112 PRESARF Other diagnosis of ARF : #PRESMUR 90 76 30 142 76 0 1 112 PRESMUR Murmur on clinical exam : #PRESPREG 1 77 30 40 77 0 1 112 PRESPREG During pregnancy : #PRESSTROK 41 77 30 89 77 0 1 112 PRESSTROK Stroke or embolism : #PRESCCF 90 77 30 142 77 0 1 112 PRESCCF Cardiac failure : #PRESAF 1 78 30 40 78 0 1 112 PRESAF Atrial fibrillation/SVT : #PRESIE 41 78 30 89 78 0 1 112 PRESIE Endocarditis : #PRESSCRE 90 78 30 142 78 0 1 112 PRESSCRE Screening : #PRESOTHER 1 79 30 40 79 0 1 112 PRESOTHER Other : #RECURRENCE 1 81 30 50 81 0 1 112 RECURRENCE Number of recurrences? : _Label77 51 81 30 0 0 0 0 112 0 = 0 1 = 1 2 = 2 3 = >3 9 = Unknown _Label78 1 83 30 0 0 0 0 112 ---> Complications since presentation? 0 = No 1 _Label79 81 83 30 0 0 0 0 112 = Yes #COMPLICSUR 1 84 30 40 84 0 1 112 COMPLICSUR Heart valve surgery : #COMPLICTHR 41 84 30 90 84 0 1 112 COMPLICTHR Thrombosis of prosthesis : #COMPLICSTR 91 84 30 142 84 0 1 112 COMPLICSTR Stroke or embolism : #COMPLICCCF 1 85 30 40 85 0 1 112 COMPLICCCF Cardiac failure : #COMPLICAF 41 85 30 90 85 0 1 112 COMPLICAF Atrial fibrillation/SVT : #COMPLICIE 91 85 30 142 85 0 1 112 COMPLICIE Endocarditis : #COMPLICOTH 1 86 30 40 86 0 1 112 COMPLICOTH Other : #PROVINCE 1 88 30 50 88 0 2 112 PROVINCE Province of Residence : _Label80 52 88 30 0 0 0 0 112 1 = Suva 2 = Ba 3 = Bua 4 = _Label81 132 88 30 0 0 0 0 112 Cakaudrove _Label82 1 89 30 0 0 0 0 112 _Label83 81 89 30 0 0 0 0 112 5 = Kadavu 6 = Lau 7 = Lomaiviti 8 = Macuata _Label84 1 90 30 0 0 0 0 112 _Label85 81 90 30 0 0 0 0 112 9 = Nadroga 10 = Navosa 11 = Naitasiri 12 = Namosi _Label86 1 91 30 0 0 0 0 112 _Label87 81 91 30 0 0 0 0 112 13 = Ra 14 = Rewa 15 = Serua 16 = Tailevu _Label88 1 92 30 0 0 0 0 112 _Label89 81 92 30 0 0 0 0 112 17 = Rotuma 99 = Unknown _Label90 1 95 30 0 0 0 0 112 ================================================================================ _Label91 81 95 30 0 0 0 0 112 ========================================================================== _Label92 1 96 30 0 0 0 0 112 Pacific Islands RHD Genetics Network CRF Cases Version: 2.5 _Label93 1 97 30 0 0 0 0 112 Database last updated 16/7/13 TP